Friday, January 27, 2017

Poland Syndrome- A Rare Congenital Disorder.

A 13 years old male came to radiology department for X-ray chest with history of cough for one month. His X- Ray is shown below:

Description: Chest X-ray  shows relative translucency of left hemithorax (or increased whiteness of right hemithorax) with mild scoliosis and pseudodextrocardia.

A CT scan was advised which is shown below:

Description: CT chest shows deficient muscle mass (pectoralis major muscle) in left hemithorax (white arrow) as the cause of abnormal X-ray chest and was diagnosed as Poland’s disease. The pectoralis muscle mass is normal on right side (black arrow).

Case Discussion:

Poland Syndrome: In Poland’s syndrome the etiology is not known and is described as an absence or hypoplasia of the pectoralis muscle on one side of the body with cutaneous syndactyly (webbing of the fingers) of the hand on the same side. Rib anomalies may also be associated.
It is a rare congenital condition.

The severity of Poland’s syndrome is variable and is often not diagnosed.
Poland’s syndrome is three times more common in males and affects the right side of the body twice as often as the left. The reasons for these differences are unknown, so is the cause.

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